- ... II trial, 34 patients with metastatic or locally advanced malignant PEComas were treated with sirolimus protein-bound particles for ...
- ... angiomyolipoma (also called perivascular epithelioid cell tumor or PEComa), which is associated with aggressive or malignant behavior and expresses melanocyte and smooth muscle markers.[ ...
- ... which the epithelial elements appear benign within a malignant mesenchymal background. Embryonal botryoides or rhabdomyosarcomas, which are found almost exclusively in infants. PEComa—a perivascular epithelial-cell tumor that may behave ...
- ... to treat recurrent desmoplastic small round cell tumors , PEComas, and epithelioid hemangioendothelioma and are being studied to treat malignant peripheral nerve sheath tumor . Sirolimus and temsirolimus are ...
- ... 800 Smooth Muscle Tumor C04.557.450.692 Perivascular Epithelioid Cell Neoplasms C04.557.450.692.249 Angiomyolipoma C04.557. ... 390 Hemangiosarcoma C04.557.450.795.400 Histiocytoma, Malignant Fibrous C04.557.450.795.455 Leiomyosarcoma C04. ...
- ... peak exposure peau d'orange PEB PEB regimen PEComa PediaSure pediatric pediatric cancer pediatric gastroenterologist pediatric hematologist ...
- ... 21 , 22 ] Inflammatory myofibroblastic tumor ALK inhibitors [ 23 ] PEComa mTOR inhibitors [ 24 ], including nab-sirolimus [ 25 ] NTRK - ... anaplastic lymphoma kinase; mTOR = mammalian target of rapamycin; PEComa = perivascular epithelioid cell tumor; TKI = tyrosine kinase inhibitor. ...