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10 results
  1. Clinical evidence tables - The Prevention and Management of Pressure Ulcers in Primary and Secondary Care - NCBI ... 
    https://www.ncbi.nlm.nih.gov/books/NBK333143
    ... Lerebours E, Kern J, et al. Efficacy and safety of ornithine alpha-ketoglutarate in heel pressure ulcers in elderly patients: results ...
  2. Nutrition and hydration - The Prevention and Management of Pressure Ulcers in Primary and Secondary Care - NCBI ... 
    https://www.ncbi.nlm.nih.gov/books/NBK333165
    ... of life 5.2.5.1.11. Ornithine alpha-ketoglutarate versus placebo One study (n=160) showed there is potentially no clinical difference between ornithine alpha-ketoglutarate and placebo for rate of complete healing of ...
  3. SLC25A19-Related Thiamine Metabolism Dysfunction - GeneReviews® - NCBI Bookshelf 
    https://www.ncbi.nlm.nih.gov/books/NBK1365
    ... a finding in other genetically defined microcephaly syndromes. Alpha-ketoglutarate. Among other genetic malformation syndromes, a similar level ... DLD Dihydrolipoamide dehydrogenase deficiency AR ↑ levels of urinary alpha-ketoglutarate may be seen in persons w/pathogenic variants ...
  4. xmlghr-summaries.xml 
    https://medlineplus.gov/download/ghr-summaries.xml
    ... or third month of life. A compound called alpha-ketoglutaric acid can be detected in their urine (alpha-ketoglutaric ... disease</synonym><synonym >Familial hyperlysinemia</synonym><synonym ... disease</synonym><synonym >Saccharopine dehydrogenase deficiency ...
  5. Childhood Acute Myeloid Leukemia Treatment (PDQ®) - PDQ Cancer Information Summaries - NCBI Bookshelf 
    https://www.ncbi.nlm.nih.gov/books/NBK66019
    ... a novel enzymatic activity that promotes conversion of alpha-ketoglutarate to 2-hydroxyglutarate.[ 187 , 188 ] This novel activity ... IDH2 mutations is a neomorphic enzyme activity converting alpha-ketoglutarate to 2-hydroxyglutarate. Cancer Cell 17 (3): 225- ...
  6. Nuclear Gene-Encoded Leigh Syndrome Spectrum Overview - GeneReviews® - NCBI Bookshelf 
    https://www.ncbi.nlm.nih.gov/books/NBK320989
    ... glycosylation defect Riley et al [2017] α-KGDH = alpha-ketoglutarate dehydrogenase; AR = autosomal recessive; BCAA = branched-chain amino ... Leigh disease with secondary deficiency for pyruvate and alpha-ketoglutarate dehydrogenase. Orphanet J Rare Dis. 2013; 8 :192. [ ...
  7. Maple Syrup Urine Disease - GeneReviews® - NCBI Bookshelf 
    https://www.ncbi.nlm.nih.gov/books/NBK1319
    ... of BCKD is shared with the pyruvate and alpha-ketoglutarate dehydrogenase complexes, and MSUD type 3 is characterized by increased urinary excretion of BCKAs and alpha-ketoglutarate accompanied by elevated plasma concentrations of lactate, pyruvate, ...
  8. References - Cirrhosis in Over 16s - NCBI Bookshelf 
    https://www.ncbi.nlm.nih.gov/books/NBK385202
    ... GR, Tacconi C, Zoli G. Use of pyridoxine-alpha-ketoglutarate (PAK) in hepatic encephalopathy. International Journal of Clinical ... Garcia-Ramos G, Fernandez-Zertuche M. Efficacy and safety of L-ornithine-L-aspartate (LOLA) administration. Open ...
  9. Dihydrolipoamide Dehydrogenase Deficiency - GeneReviews® - NCBI Bookshelf 
    https://www.ncbi.nlm.nih.gov/books/NBK220444
    ... Leigh disease with secondary deficiency for pyruvate and alpha-ketoglutarate dehydrogenase. Orphanet J Rare Dis. 2013; 8 :192. [ ...
  10. Propionic Acidemia - GeneReviews® - NCBI Bookshelf 
    https://www.ncbi.nlm.nih.gov/books/NBK92946
    ... methylcitrate as well as 3-methylcrotonylglycine, 3-hydroxybutyrate, alpha-ketoglutarate, & 3-hydroxyisovalerate. Plasma acylcarnitine profile in carbonic anhydrase ...