Skip to main content
U.S. flag

An official website of the United States government

Official websites use .gov
A .gov website belongs to an official government organization in the United States.

Secure .gov websites use HTTPS
A lock ( ) or https:// means you’ve safely connected to the .gov website. Share sensitive information only on official, secure websites.

Search help
3 results
  1. Wilms Tumor and Other Childhood Kidney Tumors Treatment (PDQ®) - PDQ Cancer Information Summaries - NCBI Bookshelf 
    https://www.ncbi.nlm.nih.gov/books/NBK65842
    ... angiomyolipoma (also called perivascular epithelioid cell tumor or PEComa), which is associated with aggressive or malignant behavior and expresses melanocyte and smooth muscle markers.[ ...
  2. Childhood Soft Tissue Sarcoma Treatment (PDQ®) - PDQ Cancer Information Summaries - NCBI Bookshelf 
    https://www.ncbi.nlm.nih.gov/books/NBK65904
    ... to treat recurrent desmoplastic small round cell tumors , PEComas, and epithelioid hemangioendothelioma and are being studied to treat malignant peripheral nerve sheath tumor . Sirolimus and temsirolimus are ...
  3. Tuberous Sclerosis Complex - GeneReviews® - NCBI Bookshelf 
    https://www.ncbi.nlm.nih.gov/books/NBK1220
    ... Badri et al 2013 ]. Perivascular epitheloid cell tumors (PEComa). In some PEComa, reported loss of either TSC2 or TSC1 [ Pan ... is evidence to support an oncogenic lineage of PEComa and angiomyolipomas in TSC. Six of 11 PEComas ...